The leftsided bochdalek hernia is more prevalent than the right one, because the rightsided dome develops earlier and the liver avoids abdominal viscera protrusion 2, 11. Bochdaleks hernia definition of bochdaleks hernia by. The majority of these cases are incidental, asymptomatic posterolateral diaphragmatic defects. The most common type is a bochdalek hernia at the side edge of the diaphragm. Ab imaging description morgagni hernia is an uncommon hernia resulting from a defect in the diaphragms attachments to the sternum and costal cartilages with herniation of abdominal content into the anterior thorax 1, 2. The aim of this study was to summarize clinically relevant data for the purpose of assisting surgeons with the workup, diagnosis, and treatment of adult patients with bochdalek hernia. In 1845, victor alexander bochdalek from prague described both right and left posterolateral cdh and it is referred as bochdalek hernia. Symptomatic bochdalek hernia in an adult europe pmc. The incidence of bochdalek and morgagni hernias among adults is very rare. Bochdalek hernia occurs from a congenital defect of the diaphragm, allowing the passage of abdominal structures into the thoracic cavity, limiting lung expansion and ventilatory function. It is more common on the left and more frequently seen in newborns and rare in adults, with over a few 100. They occur posteriorly and are due to a defect in the posterior attachment of the diaphragm when there is a failure of pleuroperitoneal membrane closure in utero. Morquio syndrome, a type of lysosomal hydrolase deficiency, results.
All irreducible hernias need immediate evaluation because of the possibility of. The purpose of this study was to determine retrospectively the prevalence and characteristics of adult bochdalek and morgagni hernias in a decade. Most hiatal hernias develop over the course of a persons life. While reflux can occur in children, having a hiatal hernia is less common. Shah sr, wishnew j, barsness k, gaines ba, potoka da, gittes gk, et al. Congenital diaphragmatic hernia cdh is a birth defect of the diaphragm. A large body of literature exists on the management of hiatal hernia. The diaphragm is the major muscle of respiration and the second most important muscle within the body after the heart. Learning radiology congenital diaphragmatic hernia. Bochdalek hernias are a very rare form of diaphragmatic hernias.
Read more about symptoms, diagnosis, treatment, complications, causes and prognosis. Synchronous morgagni and bochdalek hernias journal of. Additionally, recurrent chest infections and gastrointestinal symptoms have been reported in those with previously undiagnosed morgagni hernia. Frontal view of the chest shows a large aircontaining and walled structure in the region of the left lower lobe white arrow. Congenital diaphragmatic hernias cdh are rare congenital defects. During operations for rouxeny gastric bypass, sleeve gastrectomy and the. A bochdalek hernia is one of two forms of a congenital diaphragmatic hernia, the other form being morgagni hernia. Rarely, incarceration of hernia content may occur 3.
Malformation of the diaphragm allows the abdominal organs to push into the chest cavity, hindering proper lung formation cdh is a lifethreatening pathology in. A hernia is defined as the protrusion of an organ through an opening located on the structure that contains the organ. However, hernias during the adulthood through the right dome are more frequent, appearing incidentally in 68% of diagnoses and affects mostly the females. Pdf background congenital diaphragmatic hernia cdh is a congenital. The chest roentgenographic appearance was diagnostic in 87.
The vast majority of bochdalek hernias occurring in adults are inconsequential 1, 2. Bochdalek hernia it also known as postero lateral diaphragmatichernia, is most common chd. When compared to bochdalek hernias, morgagni hernias are. Bochdalek hernia definition of bochdalek hernia by. There are no robust studies that reveal the true natural history of this disease process.
A bochdalek hernia is a congenital abnormality in which an opening exists in the infants diaphragm, allowing normally intraabdominal organs particularly the. Morgagni hernias are even rarer and are a failure of the front of the diaphragm. Bochdalek definition of bochdalek by medical dictionary. We present a case of a bilateral morgagni hernia resulting in delayed growth in a 10monthold boy. We present a case of an 88yearold woman with severe hypoxia and respiratory. Morgagni hernia is a herniation through the foramen of morgagni, a rare form of diaphragmatic hernia that was first described by morgagni after reading an autopsy in. Consequently, we demonstrated 12 patients with bochdalek and 8 patients with morgagni hernias.
Bochdalek foramen, bochdalek ganglion, bochdalek gap, foramen of bochdalek hernia. Tiruvoipati r, vinogradova y, faulkner g, sosnowski aw, firmin rk, peek. The etiology can be congenital, due to alterations in diaphragm development, or acquired as the result of surgery, trauma, or infection. Morgagni hernia is a rare form of congenital diaphragmatic hernia. Because the body relies so much on the diaphragm for respiratory function, understanding how many different diseases processes ultimately result in dysfunction of the diaphragm is vitally important. Bochdalek hernia, the most common congenital diaphragm hernia in 95% of cases, is followed by morgagni hernia and esophageal hernia 5. Congenital defects congenital diaphragmatic hernia cdh is a welldescribed condition that occurs in about 1 in 5000 live births. Bochdalek s hernia synonyms, bochdalek s hernia pronunciation, bochdalek s hernia translation, english dictionary definition of bochdalek s hernia. The aircontaining structure is seen posteriorly on the lateral view red arrow. Terada, morgagni hernia treated by reduced port surgery. Read this lesson to learn more about this specific type of hernia, common characteristics of the condition, and how to treat it.
Bochdalek hernia is common in neonates but rarely occur in adults. In this the diaphragm abnormality is characterizedby a hole in the postero lateral corner of thediaphragm, which allows passage of the abdominalviscera into the chest cavity. Guidelines for the management of hiatal hernia a sages. Congenital diaphragmatic herniacontd why does it always ascend upto the left side. Bochdalek hernia article about bochdalek hernia by the. Lack of familiarity with the typical imaging appearance of a bochdalek hernia may lead to unnecessary work up as it may be mistaken for an indeterminate mass or diaphragmatic injury. A bochdalek hernia develops when abdominal organs push through a defective location of the diaphragm and protrude into the thoracic cavity. There are fewer than 20 cases of rightsided bochdalek hernia reported in adults in the literature.
Retroperitoneal structures may prolapse through the defect, e. Anterior defects or morgagni hernias 2328% and central hernias 27% are the other types 16, 17. Pdf the incidence of bochdalek and morgagni hernias among adults is very rare. The presentation was unique due to its bilateral nature and its symptomatic compression of the. Bilateral bochdalek hernias presenting as respiratory. Posterolateral bochdalek diaphragmatic hernia in adults. Morgagni hernia is a type of congenital diaphragmatic hernia which constitutes 26% of congenital diaphragmatic hernia cases. Symptomatic bochdalek hernias in adults are relatively rare but may lead to incarcerated bowel, intraabdominal organ dysfunction, or severe pulmonary disease. Specialty medical genetics, pediatrics edit this on wikidata. A bochdalek hernia is a congenital abnormality in which an opening exists in the infants diaphragm, allowing normally intraabdominal organs particularly the stomach and intestines to protrude into the thoracic cavity. It more commonly occurs on the right due to the protective barrier effect of the heart on the left 1, 2. Urushihara n, nakagawa y, kawashima k, fukazawa t, watanabe y, todani t. Diaphragmatic hernia in adults things you didnt know. Bochdalek hernia is a type of congenital diaphragmatic hernia that typically presents in childhood the clinical manifestation of symptoms and diagnosis in adults is extremely rare.
473 153 331 577 181 941 841 1332 879 1146 280 1526 879 1522 88 850 398 979 611 533 1525 1065 1435 223 749 1457 131 1452 1206 619 132 463 639 1230 101 987 518 803 1378 8 308 116 776 1034